A case of malignant rhabdoid tumor on the face

In 1978, the malignant rhabdoid tumor was known as a sarcomatous variant of Wilm's tumor because of its histological similarities to rhabdomyosarcoma. Since then, it has been regarded as a clinico-pathologic entity which commonly occurs in childhood and shows aggressive biologic behavior. However, histologically, identical tumors have been reported in various extrarenal organs and tissues, but have turned out to have different characteristics. Therefore, whether the rhabdoid tumor was a phenotype or an entity became controversial. We report herein, a case of a malignant rhabdoid tumor on the face.