Extra-Abdominal Desmoid-Type Fibromatosis Mimicking Myxofibrosarcoma

Ye Rin Kim, Yu Sung Yoon, Hyerim Park

Research output: Contribution to journalArticlepeer-review

Abstract

A 27-year-old woman was confirmed to have extraabdominal desmoid-type fibromatosis. Desmoid-type fibromatosis is a very rare connective tissue neoplasm with the extraabdominal type even more rare. It is most commonly found in proximal structures such as shoulders, neck, chest, and extremities. There are few case reports for desmoid-type fibromatosis located in paraspinal soft tissue. We report a case of desmoid-type fibromatosis mimicking a myxofibrosarcoma. Teaching Point: Even if there are suggestive findings for malignant soft tissue tumor on radiologic evaluation, histological confirmation is necessary before surgical treatment.

Original languageEnglish
Article number2848
JournalJournal of the Belgian Society of Radiology
Volume106
Issue number1
DOIs
StatePublished - 2022

Keywords

  • desmoid
  • fibromatosis
  • magnetic resonance imaging
  • paraspinal muscle
  • soft tissue tumor

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